| 產(chǎn)品編號(hào) | IHC0143H |
| 英文名稱 | Human Desmin Ready-To-Use IHC Kit |
| 中文名稱 | 人結(jié)蛋白即用型免疫組化試劑盒 |
| 別 名 | CSM1, CSM2, DES, I79_018932, LGMD2R |
| 性 狀 | Lyophilized or Liquid |
| 種 屬 | Human |
| 應(yīng)用范圍 | Immunohistochemistry |
| 適用樣品基質(zhì) | FFPE tissue |
| 描述 | IHC0143H is a ready-to-use IHC kit for staining of Desmin. The kit provides all reagents, from antigen retrieval to cover slip mounting, that require little to no diluting or handling prior to use. Simply apply the reagents to your sample slide according to the protocol and you're steps away from obtaining high-quality IHC data. |
| 保存條件 | Please store components at the temperatures indicated on the individual tube labels. The kit is stable for 6 months from the date of receipt. |
| 注意事項(xiàng) | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 產(chǎn)品介紹 |
Defects in Desmin are the cause of desmin related cardio skeletal myopathy (CSM) also known as desmin related myopathy (DRM). CSM is characterized by skeletal muscle weakness associated with cardiac conduction blocks, arrhythmias, restrictive heart failure, and by intracytoplasmic accumulation of desmin reactive deposits in cardiac and skeletal muscle cells. A desmin related myopathy can have a distal onset, it is then known as hereditary distal myopathy (HDM). Defects in Desmin are also the cause of dilated cardiomyopathy type 1I (CMD1I). CMD1I is an autosomal form of dilated cardiomyopathy characterized by ventricular dilatation and impaired systolic function. Gene ID: 1674 |
| 產(chǎn)品圖片 |
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Immunohistochemical analysis of paraffin embedded human colon tissue slide using IHC0143H (Human Desmin IHC Kit).
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